
Posterior Scleritis with Optic Nerve Edema Presenting in a Case of Atypical Cogan’s Syndrome
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Description
Background
• Cogan’s syndrome (CS) is a rare, systemic autoimmune disorder with
ocular and auditory manifestations
• Classic form includes:
• Non-syphilitic interstitial keratitis (IK)
• Sensorineural hearing loss with vestibular symptoms resembling
Ménière's disease
• Atypical form includes:
• Broader ocular inflammation and auditory disturbances
• Absence of IK
• Time interval of more than two years between ocular and auditory
symptoms
• The exact cause remains unknown, but may be an autoimmune etiology
• Treatment focuses on aggressive immunosuppression to prevent
irreversible damage
• Summary of Report: this case describes a 37-year-old female with
progressive ocular and auditory symptoms, ultimately diagnosed with
atypical CS
Subjects
Affiliations
- California Health Sciences University College of Osteopathic Medicine